Se estudiaron pacientes adultos con drepanocitosis, seguidos entre enero de y diciembre de ; del sexo femenino y del masculino. Introducción: la drepanocitosis es una enfermedad hematológica hereditaria y crónica. Se caracteriza por anemia crónica y diferentes trastornos asociados al. CARTA AL EDITOR. Program for comprehensive sickle cell disease care in Cuba . Programa de atención a la drepanocitosis en Cuba. Prof. Eva Svarch1, Dr.

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Potencial therapeutic approaches for the treatment of vaso-occlusion in sickle cell disease. Si continua navegando, consideramos que acepta su uso.

Tel Conclusions Acute thoracic syndrome is frequent in sickle cell disease drepancoitosis is more severe in children older than 3 years. Clinical manifestations are extremely variable between individuals and at different times.

To present the casuistics of a pediatric hospital: Este tratamiento se realiza en centros especializados.

Puede ser que usted encuentre que hablar con un consejero o psiquiatra o participar de un grupo de apoyo le ayude. Results Twenty-three episodes of acute thoracic syndrome were evaluated in eight out of 12 patients with sickle cell anemia followed-up in our hospital.


Hematology, 5pp. Vea todos los ensayos en ClinicalTrials. Conclusions This study reproduces the data described in the literaturefrom countries with a high prevalence of the disease.

Specialised Social Services Eurordis directory. What You Need to Know. Las transfusiones de sangre se usan para tratar la anemia grave. Cervera Bravo a M. Physiologic decline in fetal hemoglobin parameters in drepanoctiosis with sickle cell disease: Sucede cuando una gran cantidad de drepanocitos quedan atrapados en el bazo y producen su agrandamiento repentino. The most frequent complications were in-fections and Cada persona experimenta el dolor de forma diferente.

Síntomas y tratamientos

To review the clinical manifestations, management and outcome of episodes of acute thoracic syndrome in our hospital. Key words Sickle cell anemia. The comprehensive care of SCD in Cuba provided a better quality of life. We performed a retrospective study of 22 drepanocigosis agedless than 18 years old diagnosed with sickle cell anemiabetween January and December Sickle cell anemia is a structural hemoglobinopathy inwhich morphological and physical changes in erythrocytescause vaso-occlusive episodes in various organs andtissues.

J Pediatrics,pp. Resultados Se evaluaron 23 episodios en 8 de 12 pacientes controlados por drepanocitosis. Better screening need for sickle cell and talassemia.

Orphanet: Drepanocitosis

Twenty-eight percentof the patients diagnosed before the age of 2 years presentedcomplications. We use cookies to help provide and enhance our service and tailor content and ads. Management and treatment From birth, management should integrate prevention of infections, pain and eventual complications, with social and psycho-educational support, within multidisciplinary centers that are equipped with intensive care immediate access to blood transfusion.


Otros problemas pueden incluir: Material and methods We performed a retrospective study of 22 patients agedless than 18 years old diagnosed with sickle cell anemiabetween January and December Para controlar completamente una crisis dolorosa aguda, generalmente se necesita hospitalizar a las personas. Sickle Cell in Focus Conference Laboratory diagnosis, pathophysiology and health maintenance.

Un programa educativo individualizado es un plan que le ayuda a los estudiantes a alcanzar sus metas educativas. Methods We performed a retrospective review of all the episodes of acute thoracic syndrome diagnosed at our center in patients younger than 18 years of age with sickle cell anemia. Pediatr Clin North Am, 47pp.